Reix Philippe

The expanded French compassionate programme for elexacaftor–tezacaftor–ivacaftor use in people with cystic fibrosis without a F508del CFTR variant: a real-world study

Pierre-Régis Burgel, Isabelle Sermet-Gaudelus, Emmanuelle Girodon, Isabelle Durieu, Véronique Houdouin, Camille Audousset...

The Lancet Respiratory Medicine . 12 ( 11 ) : 888-900

DOI: 10.1016/s2213-2600(24)00208-x

2024

Article dans une revue

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Lumacaftor/Ivacaftor Population Pharmacokinetics in Pediatric Patients with Cystic Fibrosis: A First Step Toward Personalized Therapy

Naïm Bouazza, Saïk Urien, Frantz Foissac, Laure Choupeaux, Gabrielle Lui, Léo Froelicher Bournaud...

Clinical Pharmacokinetics . 63 ( 3 ) : 333-342

DOI: 10.1007/s40262-023-01342-3

2024

Article dans une revue

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COBRAPed cohort: Do sensitization patterns differentiate children with severe asthma from those with a milder disease?

Stéphanie Lejeune, Naïm Bouazza, Pascale Roland Nicaise, Valérie Jolaine, Léa Roditis, Christophe Marguet...

Pediatric Allergy and Immunology . 35 ( 3 ) : e14112

DOI: 10.1111/pai.14112

2024

Article dans une revue

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Impact of COVID-19 infection on lung function and nutritional status amongst individuals with cystic fibrosis: A global cohort study

Julie Semenchuk, Yumi Naito, Susan C Charman, Siobhán B Carr, Stephanie Y Cheng, Bruce C Marshall...

Journal of Cystic Fibrosis . 23 : 815 - 822

DOI: 10.1016/j.jcf.2024.07.019

2024

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A quick access to information on influenza burden and prevention in Lyon university hospital: A prospective QR code-based information campaign in 2022–2023

Nagham Khanafer, Sylvain Oudot, Margot Maligeay, Catherine Planckaert, Camille Mena, Nadège Trehet Mandel...

Vaccine . 42 ( 21 ) : 126160

DOI: 10.1016/j.vaccine.2024.126160

2024

Article dans une revue

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Editorial: New insights into caring for pediatric patients with cystic fibrosis

Stephanie Bui, Laurence Delhaes, Gael Dournes, Philippe Reix, Michael John Fayon

Frontiers in Pediatrics . 11

DOI: 10.3389/fped.2023.1243496

2023

Article dans une revue

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Clinical problems in rare interstitial lung diseases

Camille Fletcher, Alice Hadchouel, Caroline Thumerelle, Manon Fleury, Nouha Jedidi, Myriam Benhamida...

European Respiratory Society .

2023

Poster

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Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription

Elise Dreano, Pierre Régis Burgel, Aurelie Hatton, Naim Bouazza, Benoit Chevalier, Julie Macey...

European Respiratory Journal . 62 ( 4 ) : 2300110

DOI: 10.1183/13993003.00110-2023

2023

Article dans une revue

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Population Pharmacokinetic Modeling and Dosing Simulations of Tobramycin in Pediatric Patients with Cystic Fibrosis

Antonin Praet, Laurent Bourguignon, Florence Vetele, Valentine Bréant, Charlotte Genestet, Oana Dumitrescu...

Antimicrobial Agents and Chemotherapy . 65 ( 10 ) : e0073721

DOI: 10.1128/AAC.00737-21

2021

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Using chest CT scan and unsupervised machine learning for predicting and evaluating response to lumacaftor-ivacaftor in people with cystic fibrosis

Alienor Campredon, Enzo Battistella, Clémence Martin, Isabelle Durieu, Laurent Mely, Christophe Marguet...

European Respiratory Journal . : 2101344

DOI: 10.1183/13993003.01344-2021

2021

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Diffuse alveolar haemorrhage in children: an international multicentre study

Astrid Madsen Ring, Nural Kiper, Frederik Buchvald, Ayse Tana Aslan, Roser Ayats, Ines Azevedo...

European Respiratory Society (ERS) Congress .

2021

Acte de congrès

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Real-world assessment of LCI following lumacaftor-ivacaftor initiation in adolescents and adults with cystic fibrosis

Philippe Reix, Aurélie Tatopoulos, Iulia Ioan, Muriel Le Bourgeois, Stéphanie Bui, Marie Luce Choukroun...

Journal of Cystic Fibrosis .

DOI: 10.1016/j.jcf.2021.06.002

2021

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Factors Associated with Asthma Severity in Children: Data from the French COBRAPed Cohort

Guillaume Lezmi, Stéphanie Lejeune, Isabelle Pin, Sylvain Blanchon, Naïm Bouazza, Valérie Jolaine...

Journal of Allergy and Clinical Immunology: In Practice . 9 ( 5 ) : 1969-1979

DOI: 10.1016/j.jaip.2020.12.027

2021

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Chest physiotherapy enhances detection of Pseudomonas aeruginosa in nonexpectorating children with cystic fibrosis

Christophe Marguet, Véronique Houdouin, Isabelle Pin, Philippe Reix, Frédéric Huet, Marie Mittaine...

ERJ Open Research . 7 ( 1 ) : 00513-2020

DOI: 10.1183/23120541.00513-2020

2021

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Impact of Coexistence Phenotype Between Staphylococcus aureus and Pseudomonas aeruginosa Isolates on Clinical Outcomes Among Cystic Fibrosis Patients

Paul Briaud, Sylvère Bastien, Laura Camus, Marie Boyadjian, Philippe Reix, Catherine Mainguy...

Frontiers in Cellular and Infection Microbiology . 10 : 105996

DOI: 10.3389/fcimb.2020.00266

2020

Article dans une revue

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Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function

Pierre-Régis Burgel, Isabelle Durieu, Raphaël Chiron, Laurent Mely, Anne Prevotat, Marlene Murris-Espin...

Journal of Cystic Fibrosis .

DOI: 10.1016/j.jcf.2020.06.012

2020

Article dans une revue

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Real-Life Safety and Effectiveness of Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis

Pierre-Régis Burgel, Anne Munck, Isabelle Durieu, Raphaël Chiron, Laurent Mely, Anne Prévotat...

American Journal of Respiratory and Critical Care Medicine . 201 ( 2 ) : 188-197

DOI: 10.1164/rccm.201906-1227OC

2020

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Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis

Julie Coton, Ha-Hai Le, Victor Veuillet, Perrine Janiaud, Michel Cucherat, Behrouz Kassai-Koupai...

Journal of Cystic Fibrosis . 18 ( 4 ) : 461 - 467

DOI: 10.1016/j.jcf.2019.02.003

2019

Article dans une revue

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Usefulness of bronchoalveolar lavage in a French pediatric cohort with hypersensitivity pneumonitis

Stéphanie Wanin, Clara Malka-Ruimy, Antoine Deschildre, Nadia Nathan, Gabriel Reboux, Philippe Reix...

Pediatric Pulmonology . 55 ( 1 ) : 136-140

DOI: 10.1002/ppul.24546

2019

Article dans une revue

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Health-related quality of life in children interstitial lung disease.

Nadia Nathan, Clara Lauby, Rola Abou Taam, Katia Bessaci, Jacques Brouard, Marie-Laure Dalphin...

European Respiratory Society (ERS) Congress .

2019

Acte de congrès

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Health‐related quality of life in infants and children with interstitial lung disease

Clara Lauby, Pierre-Yves Boëlle, Rola Abou Taam, Katia Bessaci, Jacques Brouard, Marie‐laure Dalphin...

Pediatric Pulmonology . 54 ( 6 ) : 828-836

DOI: 10.1002/ppul.24308

2019

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Viral respiratory tract infections in young children with cystic fibrosis: a prospective full-year seasonal study

Mathilde Eymery, Florence Morfin, Anne Doleans-Jordheim, Marie Perceval, Camille Ohlmann, Catherine Mainguy...

Virology Journal . 16 ( 1 ) : 111

DOI: 10.1186/s12985-019-1208-7

2019

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Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis

Julie Coton, Ha-Hai Le, Victor Veuillet, Perrine Janiaud, Michel Cucherat, Behrouz Kassai-Koupai...

Journal of Cystic Fibrosis .

DOI: 10.1016/j.jcf.2019.02.003

2019

Article dans une revue

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Down syndrome and pulmonary hemosiderosis: an under-recognized association

Aurelia Alimi, Jessica Taytard, Rola Abou Taam, Véronique Houdouin, Aude Forgeron, Marc Lubrano Lavadera...

European Respiratory Society (ERS) Congress .

2018

Acte de congrès

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Place de l’analyse des gènes du surfactant dans la démarche diagnostique des pneumopathies interstitielles diffuses de l’enfant et l’adulte

Nadia Nathan, Marie Legendre, Raphaël Borie, Diane Bouvry, Mickael Afanetti, Juliette Albuisson...

Assises de Génétique Humaine et Médicale .

2018

Poster

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Eosinophilic granulomatosis with polyangiitis in children: Data from the French RespiRare (R) cohort

Agnes Fina, Jean-Christophe Dubus, Antoine Tran, Jocelyne Derelle, Philippe Reix, Michael Fayon...

Pediatric Pulmonology . 53 ( 12 ) : 1640-1650

DOI: 10.1002/ppul.24089

2018

Article dans une revue

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Pulmonary hemosiderosis in children with Down syndrome: a national experience

Aurelia Alimi, Jessica Taytard, Rola Abou Taam, Véronique Houdouin, Aude Forgeron, Marc Lubrano Lavadera...

Orphanet Journal of Rare Diseases . 13 ( 1 ) : 60

DOI: 10.1186/s13023-018-0806-6

2018

Article dans une revue

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Contribution of mutations in genes of the surfactant system to idiopathic interstitial pneumonia (IIP)

Nadia Nathan, Marie Legendre, Emilie Filhol-Blin, Raphael Borie, Diane Bouvry, Mickael Afanetti...

ERS International Congress 2018 abstracts . : OA547

DOI: 10.1183/13993003.congress-2018.OA547

2018

Acte de congrès

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Functional assessment of newly identified SFTPA1 and SFTPA2 mutations in patients with idiopathic interstitial pneumonia (IIP) and lung cancer.

Nadia Nathan, Marie Legendre, Emilie Filhol-Blin, Raphaël Borie, Diane Bouvry, Caroline Kannengiesser...

uropean Respiratory Society (ERS) Congress, .

2018

Acte de congrès

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Functional assessment of newly identified SFTPA1 and SFTPA2 mutations in patients with idiopathic interstitial pneumonia (IIP) and lung cancer28th International Congress of the European-Respiratory-Society (ERS)

Nadia Nathan, Marie Legendre, Emilie Filhol-Blin, Raphael Borie, Diane Bouvry, Caroline Kannengiesser...

28th International Congress of the European-Respiratory-Society (ERS) .

DOI: 10.1183/13993003.congress-2018.PA2235

2018

Acte de congrès

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Publications

The expanded French compassionate programme for elexacaftor–tezacaftor–ivacaftor use in people with cystic fibrosis without a F508del CFTR variant: a real-world study

Lumacaftor/Ivacaftor Population Pharmacokinetics in Pediatric Patients with Cystic Fibrosis: A First Step Toward Personalized Therapy

COBRAPed cohort: Do sensitization patterns differentiate children with severe asthma from those with a milder disease?

Impact of COVID-19 infection on lung function and nutritional status amongst individuals with cystic fibrosis: A global cohort study

A quick access to information on influenza burden and prevention in Lyon university hospital: A prospective QR code-based information campaign in 2022–2023

Editorial: New insights into caring for pediatric patients with cystic fibrosis

Clinical problems in rare interstitial lung diseases

Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription

Population Pharmacokinetic Modeling and Dosing Simulations of Tobramycin in Pediatric Patients with Cystic Fibrosis

Using chest CT scan and unsupervised machine learning for predicting and evaluating response to lumacaftor-ivacaftor in people with cystic fibrosis

Diffuse alveolar haemorrhage in children: an international multicentre study

Real-world assessment of LCI following lumacaftor-ivacaftor initiation in adolescents and adults with cystic fibrosis

Factors Associated with Asthma Severity in Children: Data from the French COBRAPed Cohort

Chest physiotherapy enhances detection of Pseudomonas aeruginosa in nonexpectorating children with cystic fibrosis

Impact of Coexistence Phenotype Between Staphylococcus aureus and Pseudomonas aeruginosa Isolates on Clinical Outcomes Among Cystic Fibrosis Patients

Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function

Real-Life Safety and Effectiveness of Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis

Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis

Usefulness of bronchoalveolar lavage in a French pediatric cohort with hypersensitivity pneumonitis

Health-related quality of life in children interstitial lung disease.

Health‐related quality of life in infants and children with interstitial lung disease

Viral respiratory tract infections in young children with cystic fibrosis: a prospective full-year seasonal study

Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis

Down syndrome and pulmonary hemosiderosis: an under-recognized association

Place de l’analyse des gènes du surfactant dans la démarche diagnostique des pneumopathies interstitielles diffuses de l’enfant et l’adulte

Eosinophilic granulomatosis with polyangiitis in children: Data from the French RespiRare (R) cohort

Pulmonary hemosiderosis in children with Down syndrome: a national experience

Contribution of mutations in genes of the surfactant system to idiopathic interstitial pneumonia (IIP)

Functional assessment of newly identified SFTPA1 and SFTPA2 mutations in patients with idiopathic interstitial pneumonia (IIP) and lung cancer.

Functional assessment of newly identified SFTPA1 and SFTPA2 mutations in patients with idiopathic interstitial pneumonia (IIP) and lung cancer28th International Congress of the European-Respiratory-Society (ERS)